🏅

WHO CNS Tumour Classification 2021

The 2021 WHO Classification of Tumours of the Central Nervous System (5th edition) introduced major revisions incorporating molecular markers alongside histology. Tumour type now integrates both morphological and genomic features into a single integrated diagnosis.

Key Principle — Integrated Diagnosis

Diagnosis = Histological type + Molecular markers + WHO Grade. Example: "Glioblastoma, IDH-wildtype, WHO grade 4" — not simply graded by appearance alone.

WHO Grades I–IV
Grade I
Slow-growing, well-differentiated. Low proliferative potential. Often potentially curable by surgery alone. Examples: pilocytic astrocytoma, meningioma WHO I.
Grade II
Slow-growing but infiltrative. Low mitotic activity. Risk of malignant transformation over time. Examples: diffuse astrocytoma IDH-mutant, oligodendroglioma.
Grade III
Malignant, anaplastic. Increased mitoses, nuclear atypia. Examples: anaplastic astrocytoma IDH-mutant, anaplastic oligodendroglioma.
Grade IV
Highly malignant. Rapid proliferation, necrosis, microvascular proliferation. Examples: Glioblastoma IDH-wildtype, diffuse midline glioma H3K27-altered.

Primary vs Secondary Tumours

Primary Brain Tumours

Arise directly from brain parenchyma, meninges, or supporting structures. Account for approximately 30% of all brain tumours in adults.

Secondary (Metastatic) Brain Tumours

Most common intracranial tumours overall. Arise from systemic malignancy spreading haematogenously to the brain. The blood-brain barrier is disrupted at metastatic sites.

Common Primary Sources of Brain Metastases

Lung (most common — NSCLC, SCLC) • Breast (esp. HER2+ and triple-negative) • Melanoma (high predilection for CNS) • Renal cell carcinomaColorectal

Brain metastases are typically multiple, well-circumscribed, ring-enhancing on MRI, located at grey-white matter junction. Single metastasis may be resected.

📈

Gliomas

Glioblastoma (GBM) — Grade 4, IDH-wildtype

  • Most common and most aggressive primary brain tumour in adults
  • Median survival: 14–16 months with optimal treatment (Stupp protocol)
  • Hallmarks: pseudopalisading necrosis, microvascular proliferation
  • Ring-enhancing lesion on MRI with surrounding oedema
  • MGMT methylation (~45%) predicts better response to temozolomide

Astrocytoma — Grade 2–4, IDH-mutant

  • IDH mutation confers significantly better prognosis than IDH-wildtype at same grade
  • Grade 2: diffuse, infiltrative; Grade 3: anaplastic; Grade 4: astrocytoma IDH-mutant (distinct from GBM)
  • Median survival for IDH-mutant Grade 4: ~3–5 years

Oligodendroglioma — IDH-mutant + 1p/19q codeletion

  • Requires both IDH mutation AND 1p/19q chromosomal codeletion for diagnosis
  • Best prognosis among diffuse gliomas; highly chemosensitive (PCV regimen)
  • Grade 2 or Grade 3 (anaplastic oligodendroglioma)
🔭

Meningioma

Arise from arachnoid cap cells of meninges. Most common primary intracranial tumour in adults. Not a glioma — extra-axial (outside brain parenchyma).

  • WHO Grade I: 80–85%, benign, slow-growing, often incidental
  • WHO Grade II: atypical, higher recurrence rate (~40% at 10 years)
  • WHO Grade III: anaplastic/malignant, rare but aggressive

Surgery is curative for accessible Grade I. Observation for small asymptomatic lesions in elderly patients.

🍐

Medulloblastoma

Embryonal tumour. Most common malignant paediatric brain tumour. Arises in the posterior fossa (cerebellum/4th ventricle). Can seed the entire CSF (leptomeningeal dissemination).

  • Presents with hydrocephalus, ataxia, headache
  • Four molecular subgroups: WNT (best prognosis), SHH, Group 3, Group 4
  • Treatment: surgery + craniospinal RT + chemotherapy
  • 5-year survival: 70–80% overall; WNT subgroup >90%

Other Key Tumours

Ependymoma

Arises from ependymal cells lining ventricles and spinal canal. Graded I–III. Molecular classification now used (ZFTA fusion, YAP1 fusion, etc.). Important cause of spinal cord tumours.

Pituitary Adenoma

  • Functioning: hormone-secreting (prolactinoma most common, ACTH — Cushing's, GH — acromegaly)
  • Non-functioning: mass effect — headache, bitemporal hemianopia, hypopituitarism

CNS Lymphoma (PCNSL)

Primarily diffuse large B-cell lymphoma. Periventricular predilection. Treat with high-dose methotrexate — avoid steroids before biopsy (steroid-sensitive, will cause regression and non-diagnostic biopsy).

🔀

Spinal Cord Tumours

Location Classification

CategoryLocationExamples
ExtraduralOutside dura materMetastases (most common), lymphoma, myeloma
Intradural ExtramedullaryInside dura, outside cordMeningioma, schwannoma, neurofibroma
IntramedullaryWithin spinal cordEpendymoma (most common adult), astrocytoma

Clinical Features

  • Extradural mets: back pain (90%), may progress to cord compression (MSCC) — neurological emergency
  • MSCC signs: bilateral weakness, sensory level, sphincter dysfunction
  • Nursing action: flat bed rest, urgent MRI whole spine, high-dose dexamethasone, oncology referral within 24 hours
  • Intramedullary: central cord syndrome pattern, pain and temperature loss > proprioception
MSCC — Oncological Emergency

New back pain in cancer patient = exclude MSCC. Dexamethasone 16 mg stat, urgent MRI, RT/surgery within 24h.

📊

Symptoms by Tumour Location

LocationKey SymptomsClinical Notes
Frontal LobePersonality change, executive dysfunction, disinhibition, contralateral limb weakness (motor cortex), incontinenceOften subtle and missed early. Family may notice before patient. Dominant: expressive aphasia (Broca's area)
Temporal LobeMemory impairment, complex partial seizures, contralateral superior quadrantanopiaDominant hemisphere (usually left): Wernicke's aphasia — fluent but non-sensical speech. Mesial temporal: memory loss, deja-vu aura
Parietal LobeContralateral hemisensory loss, spatial neglect, agraphia, acalculia, apraxiaNon-dominant (usually right): hemispatial neglect — patient ignores left side. Gerstmann syndrome (dominant): finger agnosia, acalculia, agraphia, L-R disorientation
Occipital LobeContralateral homonymous hemianopia, visual hallucinations, cortical blindnessPatient may not notice visual field defect (anosognosia). Check visual fields carefully in assessment
Posterior Fossa / CerebellumIpsilateral limb ataxia, gait ataxia, dysarthria, nystagmus, intention tremorCerebellar signs are ipsilateral to lesion. Midline (vermis): truncal ataxia, wide-based gait. Risk of hydrocephalus from 4th ventricle obstruction
BrainstemMultiple cranial nerve palsies, "crossed" deficits (ipsilateral face + contralateral body), dysphagia, dysarthria, locked-in syndromeCrossed deficits pathognomonic of brainstem lesion. Often inoperable — biopsy via stereotactic approach. Diffuse intrinsic pontine glioma (DIPG) in children
Corpus CallosumAlien hand syndrome, disconnection syndromes, rapid cognitive decline"Butterfly glioma" — GBM crossing corpus callosum. Poor prognosis

Raised Intracranial Pressure (ICP)

Pathophysiology

Monro-Kellie doctrine: the skull is a rigid box. Any increase in volume (tumour + oedema) must be compensated by reduction in CSF or venous blood. Once compensatory mechanisms fail, ICP rises exponentially.

Normal ICP: 5–15 mmHg. Sustained >20 mmHg is pathological. Cerebral perfusion pressure (CPP) = MAP – ICP; target CPP >60 mmHg.

Symptoms of Raised ICP

  • Headache: worse on waking (recumbent position increases ICP), coughing, bending, Valsalva manoeuvre; progressive, bifrontal/bioccipital
  • Nausea and vomiting: vomiting without preceding nausea (projectile) — direct medullary stimulation
  • Papilloedema: blurred disc margins, venous engorgement on fundoscopy — sign of chronic raised ICP; may cause transient visual obscurations
  • Drowsiness and cognitive change: impaired consciousness as ICP rises
  • Diplopia: 6th nerve palsy — false localising sign (long intracranial course)
Cushing's Triad — Pre-Herniation Emergency

1. Hypertension (widened pulse pressure) • 2. Bradycardia (reflex) • 3. Irregular / slow respirations (Cheyne-Stokes)

This is a very late sign indicating imminent transtentorial herniation. Immediate action required.

Herniation Syndromes

  • Uncal herniation: 3rd nerve palsy — ipsilateral dilated fixed pupil ("blown pupil"), hemiplegia
  • Central/transtentorial: bilateral pupil changes, progressive decerebrate posturing
  • Tonsillar/foramen magnum: brainstem compression, sudden death

Immediate Nursing Actions

  • 30° head elevation, neutral neck alignment (no neck flexion)
  • Maintain airway, oxygen to sats >94%
  • Urgent medical review / emergency bleep
  • IV dexamethasone 8–16 mg stat (for vasogenic oedema around tumour)
  • Mannitol 20% 0.25–1 g/kg IV (osmotic diuretic) or hypertonic saline
  • Urgent CT head; consider intubation and hyperventilation (temporising)

Seizures in Brain Tumours

Seizures occur in 30–50% of patients with brain tumours (highest with low-grade gliomas in cortical locations). Can be the presenting symptom or develop during treatment.

Seizure Classification (ILAE)

  • Focal onset aware (previously simple partial): retained consciousness, localising aura (motor, sensory, autonomic, psychic)
  • Focal onset impaired awareness (previously complex partial): altered consciousness, automatisms
  • Focal to bilateral tonic-clonic: secondary generalisation
  • Generalised onset: less common with focal tumours
Status Epilepticus (>5 minutes)

Lorazepam IV/IM 4 mg (or midazolam buccal 10 mg). If no IV: midazolam buccally. Second line: levetiracetam IV, valproate IV, phenytoin IV. Refractory: ICU, propofol/midazolam infusion. Check glucose.

Prophylactic AEDs

Not routinely recommended pre-operatively unless history of seizure. Post-operatively in craniotomy patients — often levetiracetam for short period. Not recommended long-term in seizure-free patients.

👁

Neurological Assessment

Glasgow Coma Scale (GCS)

Eye opening (1–4) + Verbal response (1–5) + Motor response (1–6). Maximum 15 = fully conscious. Score <8 = intubation threshold. Document component scores (E3V4M6 = 13), not just total.

Pupil Assessment

  • Size (mm), equality, reactivity to light (direct and consensual)
  • Unequal pupils: 1mm or more difference = anisocoria — may indicate ipsilateral uncal herniation
  • Fixed dilated: 3rd nerve compression — neurological emergency
  • Pinpoint bilateral: opiate toxicity, pontine lesion

Focal Deficit Assessment

  • Limb power: MRC scale 0–5 bilaterally, compare sides
  • Pronator drift test: sensitive for subtle upper limb weakness
  • Gait assessment, facial symmetry, speech (fluency, comprehension, naming)
  • Document baseline, track changes — any new deficit = urgent review

MRI with Gadolinium

Gold standard for brain tumour imaging. Gadolinium enhancement indicates blood-brain barrier breakdown. Ring enhancement differential: GBM vs brain abscess vs metastasis vs radiation necrosis — clinical context and MR spectroscopy/perfusion used to differentiate.

🔧

Surgical Nursing — Craniotomy Care

Pre-operative Nursing

  • Baseline neurological assessment and documentation
  • Informed consent — surgeon's role; nurse ensures patient understanding
  • Dexamethasone to reduce peri-operative cerebral oedema
  • Antiepileptic medications as prescribed
  • VTE risk assessment — TED stockings; LMWH timing neurosurgery-specific
  • Blood group and save; consent for blood products
  • Skin prep — hair clipping (not shaving) reduces infection risk
  • MRI neuronavigation — patient positioning and fiducial markers

Awake Craniotomy — Special Considerations

Awake Craniotomy for Eloquent Areas

Used when tumour is in or adjacent to speech, language, or motor cortex. Patient must be awake and cooperative during tumour resection to enable continuous cortical mapping. Requires:
• Rigorous pre-operative psychological preparation
• Detailed discussion of what to expect (noise, sensations)
• Patient performs tasks: naming, reading, motor tasks
• Asleep-awake-asleep protocol or monitored anaesthesia care (MAC)
• In GCC: language considerations (Arabic, Urdu, Hindi) — neuropsychology assessment in patient's primary language essential

Post-operative Neurological Observations

Minimum Frequency: Hourly for First 24 Hours

GCS (document components) • Pupil size and reactivity bilaterally • Limb power (MRC scale) • Speech assessment • Blood pressure, HR, SpO2, temperature • Wound inspection • Drain output

  • Head positioning: 30° head elevation; neutral neck alignment; no sustained neck flexion
  • Pain: regular paracetamol; avoid NSAIDs (bleeding risk); opioids with caution (CNS depression/pupil masking)
  • Nausea: ondansetron; avoid prochlorperazine (lowers seizure threshold)
  • Temperature: normothermia target; fever >38°C increases cerebral metabolic demand
  • Blood glucose: tight control; hyperglycaemia worsens outcome (steroids often prescribed)

External Ventricular Drain (EVD)

  • Zero reference point: external auditory meatus (tragus) — represents foramen of Monro
  • Opening pressure prescribed (e.g. 10–15 cmH₂O) — drain only opens above this pressure
  • Hourly drainage documentation — colour (normal: clear/straw-coloured)
  • Cloudy/bloody CSF = send M&C, notify neurosurgery
  • Never reposition without medical order; maintain closed sterile system

VTE Prophylaxis in Neurosurgery

Brain tumour patients have very high VTE risk (Khorana score, tumour type, immobility). However, post-craniotomy LMWH timing is delayed due to intracranial bleeding risk. Typical protocol:

💉

Dexamethasone in Neuro-Oncology

Most commonly used corticosteroid in brain tumour management. Reduces vasogenic oedema by stabilising the blood-brain barrier. Does not treat the tumour itself.

Indications

  • Symptomatic peri-tumoral cerebral oedema
  • Raised ICP — emergency management
  • Post-operative cerebral oedema
  • Radiotherapy-induced oedema / pseudoprogression

Typical Regimen

  • Loading dose: 8–16 mg IV/PO (emergency: 10–16 mg IV stat)
  • Maintenance: 4 mg QDS (reducing to lowest effective dose)
  • Reducing regimen: taper slowly — do not stop abruptly (risk of adrenal insufficiency and tumour oedema rebound)

Side Effects — Nursing Monitoring

  • Hyperglycaemia: monitor blood glucose BD–QDS; sliding scale or insulin dose adjustment. In GCC: high baseline T2DM prevalence — vigilance essential
  • Steroid myopathy: proximal muscle weakness (difficulty rising from chair, climbing stairs) — delayed recognition; physiotherapy important
  • Infection: immunosuppression — PCP prophylaxis with co-trimoxazole if on dexamethasone >3 weeks concurrently with chemotherapy
  • Gastrointestinal: peptic ulceration — prescribe PPI (omeprazole/lansoprazole) concomitantly
  • Psychiatric: insomnia, mood lability, steroid psychosis (rare)
  • Cushing's syndrome: moon face, buffalo hump, striae, weight gain (chronic use)
  • Osteoporosis: bone protection (calcium/vitamin D, bisphosphonate) for prolonged use

Radiotherapy in Brain Tumours

Types of Radiotherapy

  • External Beam RT (EBRT): standard fractionated RT (e.g. 60 Gy in 30 fractions for GBM — Stupp protocol)
  • Hypofractionated RT: shorter course for elderly/poor performance (40 Gy in 15 fractions)
  • Stereotactic Radiosurgery (SRS): Gamma Knife, CyberKnife, Linac-based SRS — high-precision single/few fraction delivery to small targets (brain mets, AVM, meningioma)
  • Whole Brain RT (WBRT): for multiple brain metastases; now less favoured (neurocognitive toxicity) vs SRS; still used for leptomeningeal disease
  • Proton therapy: available in limited centres; beneficial for paediatric tumours and skull base lesions

Radiotherapy Side Effects — Nursing

  • Alopecia: hair loss in RT field; usually temporary (permanent if high dose); provide wig referral, emotional support
  • Fatigue: very common, peaks 2–4 weeks; counsel on activity pacing
  • Cerebral oedema: increased dexamethasone during RT if symptomatic
  • Skin reaction: erythema, moist desquamation — aqueous cream, avoid sun
  • Pseudoprogression: MRI may show increased enhancement 1–3 months post-RT — treatment effect, not true progression; confirm with MR perfusion/spectroscopy or repeat scan
  • Radiation necrosis: late effect (>6 months); can be symptomatic — treated with bevacizumab or hyperbaric oxygen
  • Neurocognitive effects: memory, attention impairment — especially after WBRT; memantine may provide modest protection
💊

Chemotherapy — Temozolomide (TMZ) and MGMT

Stupp Protocol for GBM

Standard of care since 2005. Concurrent chemoradiotherapy followed by adjuvant chemotherapy:

  • Phase 1: TMZ 75 mg/m² daily throughout RT (6 weeks)
  • Phase 2: 4-week break
  • Phase 3: Adjuvant TMZ 150–200 mg/m² days 1–5 of 28-day cycle × 6 cycles

MGMT Methylation

MGMT (O6-methylguanine-DNA methyltransferase) is a DNA repair enzyme. Methylation of the MGMT promoter silences the gene, preventing DNA repair after TMZ alkylation — tumour becomes more sensitive to TMZ.

  • MGMT methylated (~45% GBMs): median survival 21–23 months with TMZ
  • MGMT unmethylated: limited benefit from TMZ; clinical trials recommended

Toxicity Monitoring — Nursing

Lymphopenia Monitoring

TMZ causes lymphopenia, particularly CD4 T-cell depletion. Check FBC before each cycle. If CD4 <200 cells/μL: increased risk of Pneumocystis jirovecii pneumonia (PCP).

PCP Prophylaxis

  • Co-trimoxazole (trimethoprim/sulfamethoxazole) 960 mg 3×/week throughout concurrent chemoRT and during adjuvant TMZ
  • Alternatives for sulfa allergy: dapsone, atovaquone, pentamidine nebulisation
  • Nurse education: importance of adherence, monitoring for rash (SJS risk with co-trimoxazole)

Additional Nursing Considerations

  • Oral TMZ: take on empty stomach, 1 hour before RT; anti-emetics 30 min before
  • Safe handling of oral chemotherapy — cytotoxic precautions; do not crush capsules
  • Neutropenic sepsis protocol awareness

Seizure Management & AEDs

Anti-Epileptic Drug (AED) Choice in Brain Tumours

Levetiracetam (Keppra) — Preferred First-Line AED

Advantages: broad spectrum, no cytochrome P450 induction (critical — does not reduce chemotherapy/steroid efficacy), no therapeutic drug monitoring required, available IV for post-operative/unable to swallow, renal excretion. Side effects: mood changes/irritability ("Keppra rage") — counsel patient/family; psychiatric history screen.

Phenytoin — Why Avoid in Neuro-Oncology

  • Strong CYP3A4 inducer: significantly reduces levels of dexamethasone (may worsen oedema), TMZ, and many other drugs
  • Requires therapeutic drug monitoring (narrow therapeutic index)
  • Multiple drug interactions and adverse effects (gingival hyperplasia, hirsutism, cerebellar atrophy)
  • Still used in some emergency settings but long-term use discouraged in brain tumour patients on chemotherapy

Other AEDs Used

  • Sodium valproate: also CYP inducer — use with caution; however, HDAC inhibitor properties may have antitumour effect (under investigation)
  • Lacosamide: sodium channel blocker, few interactions, IV available
  • Brivaracetam: similar to levetiracetam, fewer psychiatric effects

Seizure Cluster / Rescue Medication

  • Home rescue: buccal midazolam 10 mg or rectal diazepam 10–20 mg
  • Educate family/carers on administration — annual competency checks
  • Epilepsy care plan — driving restrictions (DVLA/equivalent GCC authority), water safety, lifestyle advice
🧠

Cognitive Rehabilitation

Cognitive impairment in brain tumours results from tumour location, oedema, surgical injury, RT effects, and chemotherapy. Affects quality of life profoundly — often more distressing to patients than physical deficits.

Occupational Therapy Assessment

  • Cognitive screening: MoCA (Montreal Cognitive Assessment), MMSE
  • Assessment of functional cognition: medication management, cooking, finances
  • Return-to-work/driving capacity assessment
  • Memory aids: electronic reminders, diaries, smartphone apps, visual cues
  • Environmental modifications: routine, structure, simplified tasks

Communication Rehabilitation (Speech-Language Therapy)

  • Aphasia: intensive speech therapy post-surgery for dominant hemisphere tumours; constraint-induced language therapy
  • Augmentative and Alternative Communication (AAC): high-tech (tablets, eye-gaze technology) and low-tech (picture boards) for severe aphasia
  • Dysarthria: articulation exercises, voice amplifiers
  • Cultural consideration: bilingual/multilingual patients in GCC — assess in primary language; may need bilingual SLT

Driving and Legal Capacity

Important: Driving Restrictions

Any patient with brain tumour-related seizures must not drive until seizure-free for the required period (varies by country). In GCC: inform patients of legal obligations. Document advice given in nursing notes.

🏃

Mobility & Physical Rehabilitation

Physiotherapy in Neuro-Oncology

  • Early mobilisation post-craniotomy (day 1–2 post-op) — reduces VTE, deconditioning, pneumonia
  • Hemiplegia rehabilitation: task-specific training, NDT (Bobath) approach, constraint-induced movement therapy
  • Gait retraining: parallel bars, walking aids, orthoses (AFO for foot drop)
  • Spasticity management: positioning, stretching, baclofen, botulinum toxin

Falls Prevention

Brain tumour patients have very high falls risk (weakness, ataxia, seizures, cognitive impairment, steroid myopathy, fatigue). NICE falls prevention principles apply:

  • Multifactorial risk assessment on admission and after any deterioration
  • Bed rails — individual risk/benefit assessment (entrapment vs. fall prevention)
  • Safe footwear, non-slip socks, clear call bell access
  • Supervised mobility; 1:1 nursing for seizure-prone patients
  • Medication review (sedating AEDs, opioids, steroids)

Cancer-Related Fatigue Management

  • Most common symptom — multifactorial (disease, treatment, anaemia, psychological)
  • Activity pacing: plan activities around energy peaks; balance rest and activity
  • Aerobic exercise: moderate-intensity exercise is evidence-based (ASCO guidelines) — even in brain tumour patients; improves fatigue, mood, cognitive function
  • Treat contributing factors: anaemia (check FBC), hypothyroidism, depression, sleep disturbance
  • Exclude disease progression if fatigue suddenly worsens
💕

Psychological Support

Prevalence of Psychological Morbidity

Depression and anxiety are significantly more prevalent in brain tumour patients than other cancer populations. Rates of clinically significant depression: 30–45%. Anxiety: 30–40%. Contributing factors: uncertainty of prognosis, cognitive changes, loss of independence, role changes, fear of seizures.

Screening

  • PHQ-9 for depression, GAD-7 for anxiety — validated in neuro-oncology
  • HADS (Hospital Anxiety and Depression Scale) — brief, widely used
  • Screen at diagnosis, after significant treatment events, and at disease progression

Interventions

  • Psychological therapy (CBT) — delivered by neuro-oncology psychologist; telehealth expanding access in GCC
  • Antidepressants: SSRIs preferred; avoid bupropion (lowers seizure threshold)
  • Peer support: brain tumour support groups; Brainstrust (UK), CBTF, regional GCC organisations
  • Social work: financial concerns, work, family relationships

Caregiver Burden

Family caregivers of brain tumour patients experience exceptionally high burden due to personality and behavioural changes (frontal lobe effects), cognitive changes, seizures, and the prolonged trajectory. Offer:

  • Carer needs assessment — separate from patient assessment
  • Respite care planning
  • Carer support groups and counselling
  • Practical information about the disease (empowers caregivers)

Corticosteroid Weaning — Symptom Interpretation

Progression vs. Steroid Reduction

Symptom deterioration during dexamethasone weaning may indicate: (1) disease progression — rescan, or (2) steroid withdrawal — increase dose temporarily then wean more slowly. Clinical assessment and imaging guide decision. Avoid abrupt cessation.

🕯

GBM Disease Trajectory & End-of-Life Recognition

Typical GBM Trajectory

GBM median survival 14–16 months from diagnosis (Stupp protocol). Trajectory is relatively predictable but sudden deterioration can occur from seizures, haemorrhage, or hydrocephalus.

  • Diagnosis to treatment: 2–4 weeks (surgery + recovery)
  • Chemoradiotherapy phase: 6 weeks (relatively functional)
  • Adjuvant chemotherapy: 6 cycles (~6 months)
  • Progression/second-line treatment: median 3–6 months
  • Terminal phase: typically 2–3 weeks of rapid decline once KPS drops below 50
Early Advance Care Planning

Unlike many cancers, GBM may cause cognitive impairment early, limiting capacity. ACP conversations must begin early, while capacity is preserved. Do not defer until decline — by then patient may lack capacity to express preferences.

Recognising the End-of-Life Phase

Clinical indicators of the last weeks/days in GBM:

  • Declining function: Karnofsky Performance Score <50 (<50% = requires assistance with most activities)
  • Increasing seizure frequency or first seizures in previously seizure-free patients
  • Progressive dysphagia: unable to swallow medications safely
  • Increasing drowsiness: sleeping most of the day
  • Progressive neurological deficits: new focal signs, increasing hemiplegia
  • Reduced oral intake: disinterest in food and fluids
  • Cognitive deterioration: confusion, disorientation

The 2–3 week rapid decline pattern is characteristic of GBM end-of-life. Families should be gently prepared for this trajectory.

📋

Advance Care Planning

Timing

ACP should begin at the earliest appropriate opportunity — often at point of diagnosis or soon after. Check mental capacity at each conversation. Document clearly.

Key ACP Components

  • Understanding of diagnosis/prognosis: what does the patient know and want to know?
  • Priorities and values: what matters most to the patient?
  • Preferred place of care/death: home, hospice, hospital? (GCC: many patients and families prefer hospital — explore this without assumption)
  • Advance Statement: written expression of wishes (not legally binding but guides care)
  • Advance Decision to Refuse Treatment (ADRT): legally binding refusal of specific treatments
  • DNACPR: do-not-attempt cardiopulmonary resuscitation — discuss timing (avoid too early in trajectory; avoid too late when patient lacks capacity)
  • Lasting Power of Attorney: health and welfare LPA — who makes decisions if patient loses capacity?

DNACPR Discussion

In GBM, DNACPR is appropriate to discuss when KPS <50 or at progression on second-line treatment. Frame as: "If your heart were to stop, CPR is very unlikely to restart it given your illness, and we want to focus on comfort." Document sensitively. In GCC: cultural and religious context (Islamic perspective on prolonging life vs. allowing natural death — engage with chaplaincy/family).

Symptom Management at End of Life

Withdrawing Dexamethasone

Dexamethasone at End of Life — Individual Assessment

Benefits: reduces cerebral oedema, may briefly improve neurological function and comfort. Harms at end of life: Cushing's syndrome, infections, hyperglycaemia, proximal weakness, insomnia.

If patient is in last days of life, is unconscious, or there is no benefit evident: taper and discontinue. If maintaining comfort, continue at lowest effective dose via SC if oral route lost.

Terminal Seizures — Anticipatory Prescribing

Seizures are common in the last days of GBM. Anticipatory medications must be prescribed and readily available:

  • Midazolam 2.5–10 mg buccal/SC — first-line for acute seizure in dying patient
  • Midazolam SC infusion (syringe driver) for seizure prevention/sedation
  • Levomepromazine SC for agitation/distress
  • Phenobarbitone SC for refractory seizures (specialist palliative care)
  • Nurse education: anticipatory prescribing protocols — nurses can administer when patient deteriorates suddenly; do not wait for doctor to prescribe

Dysphagia and Route of Medication

  • When swallowing becomes unsafe: switch to subcutaneous (SC) route via syringe driver
  • Review all medications: what is essential for comfort? Stop non-essential drugs
  • CANH (Clinically Assisted Nutrition and Hydration): ethical decision; evidence does not support routine artificial hydration in dying brain tumour patients; family discussion essential; focus on mouth care

Family Support

Brain Tumour Behavioural Changes — Family Grief

Frontal lobe disinhibition, personality changes, and cognitive decline cause profound grief and distress for families — often described as "losing the person before they die" (pre-death grief/anticipatory grief). Nursing role: validate these feelings, explain the neurological basis, offer specialist psychological support, and connect with brain tumour support organisations.

🏠

Place of Death and Syringe Driver Nursing

Syringe Driver Management

  • Subcutaneous infusion over 24 hours — maintains consistent drug levels
  • Common drugs: morphine/oxycodone (pain), midazolam (seizures/anxiety), levomepromazine (agitation/nausea), hyoscine butylbromide (secretions)
  • Check site 4-hourly: redness, swelling, leakage
  • Check driver rate, volume remaining, battery every nursing round
  • Drug compatibility: check with pharmacist (not all combinations compatible)
  • Document: drug batch numbers, site, any PRN medications administered

Last Days of Life Nursing Care

  • Mouth care: regular oral care every 1–2 hours; foam swabs, petroleum jelly for lips
  • Skin care: pressure area care; turning 2–4 hourly if possible; appropriate pressure mattress
  • Comfort positioning: semi-recumbent; do not force flat (ICP) unless unconscious and comfortable
  • Eye care: lubricating eye drops if eyes open (corneal drying)
  • Noise: reduce ward noise; allow family at bedside; explain signs of approaching death (changes in breathing, mottling, cooling extremities)
  • Document: ceiling of care clearly in nursing notes and care plan; confirm DNACPR in place and documented
🌎

Neuro-Oncology in the GCC

Epidemiology

Brain tumour incidence in the GCC mirrors global trends but with regional considerations. Brain and CNS cancers represent approximately 1.5–2.5% of all cancer diagnoses in GCC countries. GBM remains the most common malignant primary brain tumour across the region.

  • Higher rates of consanguinity in some GCC populations may influence genetic predisposition to certain tumours
  • Diagnosis often later due to variation in healthcare access and symptom attribution
  • Rapidly expanding neurosurgical and radiation oncology capacity across the region

Key Neurosurgical Centres — GCC

CentreCountryCapability
King Fahd Medical City (KFMC)Saudi ArabiaComprehensive neuro-oncology, Gamma Knife SRS, awake craniotomy
King Faisal Specialist Hospital & Research Centre (KFSH&RC)Saudi ArabiaTertiary neurosurgery, proton therapy, molecular tumour board
Cleveland Clinic Abu DhabiUAEFull neuro-oncology programme, Gamma Knife, CyberKnife
Hamad Medical Corporation (HMC)QatarNational Neuroscience Institute, comprehensive neuro-oncology
American Hospital Dubai / Mediclinic CityUAENeurosurgery, stereotactic procedures
Royal Hospital OmanOmanNational tertiary neurosurgery centre
🏃

GCC-Specific Clinical Considerations

Awake Craniotomy — Cultural Considerations

  • Language: patient must be able to communicate during procedure. In GCC, patients may speak Arabic (multiple dialects), Urdu, Hindi, Tagalog, Malayalam, English — neuropsychology assessment must be conducted in patient's primary language
  • Religious observance: prayer times, fasting (Ramadan) — surgical scheduling considerations; reassure patients that Islamic scholars permit medical necessity during Ramadan
  • Gender considerations: some female patients may prefer female surgical/nursing team members where possible; document preferences and accommodate where feasible
  • Family involvement: GCC cultures value family-centred decision making; while legal consent is individual, involve family where appropriate and consented to by patient

Steroid-Induced Hyperglycaemia in GCC

High Baseline Diabetes Prevalence

GCC countries have among the highest T2DM prevalence globally (UAE ~19%, Saudi Arabia ~18%, Qatar ~16%). Dexamethasone significantly worsens glycaemic control. Monitor blood glucose QDS during dexamethasone use. Proactive insulin prescribing is often required. Liaise with endocrinology/diabetes team early.

Regulatory Frameworks for Neuro-Oncology Nurses

  • DHA (Dubai Health Authority): license categories include Registered Nurse — specialty endorsement available
  • DOH (Department of Health — Abu Dhabi): oncology nursing scope of practice guidelines
  • SCFHS (Saudi Commission for Health Specialties): oncology nursing classification; relevant exam domains include neuro-oncology pharmacology and symptom management
  • MOH Kuwait / Oman MOH / NHRA Bahrain: varying neuro-oncology nursing frameworks — check current standards

Raised ICP Early Warning Tool

Clinical decision support tool for nursing assessment of patients with brain tumours. Answer each question based on current clinical findings, then calculate the ICP concern level.

⚠ ICP Assessment Tool — Neuro-Oncology

🎓

MCQ Practice — Neuro-Oncology Nursing (DHA/DOH/SCFHS)

Click on an answer to reveal whether it is correct and the explanation.

1. A patient with GBM is prescribed dexamethasone 4 mg QDS. Which monitoring parameter is most critical due to the specific context of GCC patients?
  • A. Daily weight measurement
  • B. Blood glucose monitoring QDS
  • C. 24-hour urine collection
  • D. Serum sodium daily
Correct: B. GCC countries have among the world's highest T2DM prevalence (~16–19%). Dexamethasone causes significant steroid-induced hyperglycaemia, particularly problematic in this population. QDS blood glucose monitoring is essential, and proactive insulin prescribing is often required.
2. Which molecular feature of GBM predicts a better response to Temozolomide (TMZ)?
  • A. IDH-wildtype status
  • B. 1p/19q codeletion
  • C. MGMT promoter methylation
  • D. EGFR amplification
Correct: C. MGMT methylation silences the MGMT DNA repair gene, preventing the tumour from repairing the DNA damage caused by TMZ alkylation. Patients with MGMT-methylated GBM have median survival of 21–23 months vs 12–14 months without methylation.
3. A post-craniotomy patient develops a fixed, dilated right pupil with left hemiplegia. What is the priority nursing action?
  • A. Repeat neuro obs in 30 minutes
  • B. Administer prescribed analgesia and reassess
  • C. Emergency bleep/call neurosurgery immediately — signs of uncal herniation
  • D. Position patient flat and document findings
Correct: C. A fixed dilated pupil (3rd nerve compression) with contralateral hemiplegia indicates uncal transtentorial herniation — a neurosurgical emergency. Immediate emergency call, maintain airway, 30° head elevation, alert team for urgent CT and possible return to theatre.
4. Why is levetiracetam the preferred anti-epileptic drug in brain tumour patients receiving chemotherapy?
  • A. It requires therapeutic drug monitoring ensuring safe levels
  • B. It does not induce CYP450 enzymes and therefore does not reduce chemotherapy efficacy
  • C. It has no neuropsychiatric side effects
  • D. It crosses the blood-brain barrier more effectively than other AEDs
Correct: B. Levetiracetam does not induce CYP450 enzymes, making it ideal for concurrent use with chemotherapy (e.g. TMZ) and dexamethasone. Phenytoin is a strong CYP inducer that would significantly reduce serum levels of many chemotherapy agents. Note: levetiracetam can cause mood changes/irritability ("Keppra rage") — inform patients and families.
5. During awake craniotomy for a dominant hemisphere glioma, the patient suddenly cannot name objects when asked. What does this indicate and what should happen?
  • A. The patient is anxious — reassure and continue resection
  • B. The patient needs more sedation — contact anaesthetist
  • C. The surgeon is stimulating/resecting eloquent speech cortex — stop resection at this site
  • D. Seizure activity — administer IV levetiracetam immediately
Correct: C. In awake craniotomy with cortical mapping, continuous language tasks identify eloquent cortex. If the patient loses language during stimulation/resection, this is a positive mapping response indicating the surgeon is at or near Broca's/Wernicke's area. Resection stops at this point to preserve function. This is the entire purpose of the awake approach.
6. A GBM patient on concurrent TMZ and RT develops a CD4 count of 180 cells/μL. What prophylaxis is indicated?
  • A. Aciclovir for HSV prophylaxis
  • B. Co-trimoxazole for Pneumocystis jirovecii pneumonia (PCP) prophylaxis
  • C. Fluconazole for Candida prophylaxis
  • D. Isoniazid for TB prophylaxis
Correct: B. TMZ causes lymphopenia and CD4 depletion. When CD4 falls below 200 cells/μL (or is <200 at any point during concurrent chemoRT), PCP prophylaxis with co-trimoxazole (960 mg 3× weekly) is indicated. PCP in this setting carries significant mortality risk. If sulfa-allergic: dapsone or atovaquone.
7. Which finding on fundoscopy suggests raised intracranial pressure?
  • A. Arteriovenous nipping
  • B. Papilloedema (blurred disc margins with venous engorgement)
  • C. Flame-shaped haemorrhages
  • D. Cotton wool spots
Correct: B. Papilloedema — swelling of the optic disc due to raised ICP transmitted along the optic nerve sheath — manifests as blurred disc margins, elevation of the disc, venous engorgement, and loss of spontaneous venous pulsation. It indicates chronic raised ICP. AV nipping indicates hypertensive retinopathy.
8. An oligodendroglioma requires which two molecular features for definitive WHO 2021 diagnosis?
  • A. IDH-wildtype and EGFR amplification
  • B. MGMT methylation and H3K27M mutation
  • C. IDH mutation AND 1p/19q codeletion
  • D. TERT promoter mutation and ATRX loss
Correct: C. Per WHO CNS 2021, oligodendroglioma requires BOTH IDH mutation AND 1p/19q chromosomal codeletion. The presence of both defines this tumour type regardless of histological appearance. Oligodendroglioma has the best prognosis among diffuse gliomas and is highly chemosensitive (PCV — procarbazine, CCNU, vincristine).
9. In GBM end-of-life care, a patient becomes increasingly drowsy and unable to swallow. Their dexamethasone is currently 2 mg BD. What is the most appropriate action?
  • A. Increase dexamethasone to 8 mg via NG tube to improve level of consciousness
  • B. Stop dexamethasone immediately
  • C. Review clinical benefit vs. harm; consider continuing via SC route if beneficial, or tapering to cessation if in last days of life
  • D. Convert to oral prednisolone via NG tube
Correct: C. Dexamethasone decisions at end of life require careful individual assessment. If the patient is clearly in the last days of life with no reversible component, dexamethasone should be tapered and stopped (the harms — Cushing's, infection, hyperglycaemia — outweigh benefits). If there is uncertainty, a trial via SC route may be appropriate. Abrupt cessation risks adrenal crisis and rebound oedema.
10. Which brain tumour location characteristically produces "crossed" neurological deficits (ipsilateral cranial nerve palsy + contralateral limb weakness)?
  • A. Frontal lobe
  • B. Temporal lobe
  • C. Thalamus
  • D. Brainstem
Correct: D. Brainstem lesions produce crossed deficits because cranial nerve nuclei are ipsilateral to the lesion while descending motor tracts decussate below the brainstem. Classic example: right-sided facial palsy (ipsilateral CN VII palsy from pontine lesion) + left hemiplegia (contralateral corticospinal tract). This pattern is pathognomonic of a brainstem lesion.